专题：Amyloidosis: Diagnosis, Treatment, Outcomes

This cluster of papers focuses on the molecular mechanisms, diagnosis, treatment, and prognosis of amyloidosis, with a particular emphasis on transthyretin-related cardiac and familial amyloid polyneuropathy. It covers topics such as RNAi therapy, cardiovascular magnetic resonance, and immunoglobulin light chain involvement.
最新文献
Probing the surrogate validity of proteinuria thresholds in C3 glomerulopathy/immune-complex membranoproliferative glomerulonephritis: unresolved biases and mechanistic gaps

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Mass spectrometry footprinting reveals how kinetic stabilizers counteract transthyretin dynamics altered by pathogenic mutations

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Monitoring heart involvement in treated and untreated transthyretin amyloidosis

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Localized cutaneous nodular amyloidosis from insulin injections in a 40-year-old woman

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Real-World Efficacy of Tafamidis in Korean ATTR-CM Patients: A Retrospective Observational Strain Analysis

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Parameters Associated With Renal Recovery and Survival in Myeloma Patients With Acute Renal Failure to Cast Nephropathy

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Tiger Man Sign in Sarcoid Myopathy

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Revisiting the genetic epidemiology of ATTRv in Spain: the Balearic Islands as a high-prevalence founder focus

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Progression of QRS duration – a potential surrogate marker of survival in ATTRwt amyloidosis patients

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First case report of talquetamab use in AL amyloidosis

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近5年高被引文献
2023 ACC Expert Consensus Decision Pathway on Comprehensive Multidisciplinary Care for the Patient With Cardiac Amyloidosis

article Full Text OpenAlex 457 FWCI84.85137629

Performance of plasma phosphorylated tau 181 and 217 in the community

article Full Text OpenAlex 446 FWCI96.45974903

Efficacy and Safety of Acoramidis in Transthyretin Amyloid Cardiomyopathy

article Full Text OpenAlex 338 FWCI161.36306764

Efficacy and safety of vutrisiran for patients with hereditary transthyretin-mediated amyloidosis with polyneuropathy: a randomized clinical trial

article Full Text OpenAlex 328 FWCI39.62826887

Amyloid nomenclature 2022: update, novel proteins, and recommendations by the International Society of Amyloidosis (ISA) Nomenclature Committee

article Full Text OpenAlex 298 FWCI36.3054016

Vutrisiran in Patients with Transthyretin Amyloidosis with Cardiomyopathy

article Full Text OpenAlex 260 FWCI124.86427853

Amyloid-related imaging abnormalities (ARIA): radiological, biological and clinical characteristics

review Full Text OpenAlex 259 FWCI77.05189501

Patisiran Treatment in Patients with Transthyretin Cardiac Amyloidosis

article Full Text OpenAlex 252 FWCI46.41760191

Extramedullary disease in multiple myeloma: a systematic literature review

review Full Text OpenAlex 239 FWCI52.76904604

Phase 1 Trial of Antibody NI006 for Depletion of Cardiac Transthyretin Amyloid

article Full Text OpenAlex 204 FWCI37.69109275